PUBLICATIONSDataCNSNeuroDegeneration
octubre 5, 2021
Disulfide cross-linked multimers of TDP-43 and spinal motoneuron loss in a TDP-43A315T ALS/FTD mouse model.
Bargsted L, Medinas DB, Martínez Traub F, Rozas P, Muñoz N, Nassif M, Jerez C, Catenaccio A, Court FA, Hetz C, Matus S.
Sci Rep. 2017 Oct 27;7(1):14266. doi: 10.1038/s41598-017-14399-5.
PMID: 29079747
PUBLICATIONSReviewPNSCNSNeuroDegenerationNeuroRegeneration
octubre 5, 2021
Injury to the nervous system: A look into the ER.
Valenzuela V, Oñate M, Hetz C, Court FA.
Brain Res. 2016 Oct 1;1648(Pt B):617-625. doi: 10.1016/j.brainres.2016.04.053. Epub 2016 Apr 23.
PMID: 27117870
PUBLICATIONSDataCNSNeuroDegeneration
octubre 5, 2021
Microtubule-associated protein 1B (MAP1B)-deficient neurons show structural presynaptic deficiencies in vitro and altered presynaptic physiology.
Bodaleo FJ, Montenegro-Venegas C, Henríquez DR, Court FA, Gonzalez-Billault C.
Sci Rep. 2016 Jul 18;6:30069. doi: 10.1038/srep30069.
PMID: 27425640
PUBLICATIONSDataPNSCNSNeuroDegeneration
octubre 5, 2021
Reactive oxygen species trigger motoneuron death in non-cell-autonomous models of ALS through activation of c-Abl signaling.
Rojas F, Gonzalez D, Cortes N, Ampuero E, Hernández DE, Fritz E, Abarzua S, Martinez A, Elorza AA, Alvarez A, Court F, van Zundert B.
Front Cell Neurosci. 2015 Jun 9;9:203. doi: 10.3389/fncel.2015.00203. eCollection 2015.
PMID: 26106294
PUBLICATIONSDataNervous System FxPNSCNS
octubre 4, 2021
The p75 neurotrophin receptor evades the endolysosomal route, favouring multivesicular bodies specialised for exosomal release in neuronal cells.
Escudero CA, Lazo OM, Galleguillos C, Parraguez JI, Lopez-Verrilli MA, Cabeza C, Leon L, Saeed U, Retamal C, Gonzalez A, Marzolo MP, Carter BD, Court FA, Bronfman FC.
J Cell Sci. 2014 May 1;127(Pt 9):1966-79. doi: 10.1242/jcs.141754. Epub 2014 Feb 25.
PMID: 24569882
octubre 4, 2021
Control of dopaminergic neuron survival by the unfolded protein response transcription factor XBP1.
Valdés P, Mercado G, Vidal RL, Molina C, Parsons G, Court FA, Martinez A, Galleguillos D, Armentano D, Schneider BL, Hetz C.
Proc Natl Acad Sci U S A. 2014 May 6;111(18):6804-9. doi: 10.1073/pnas.1321845111. Epub 2014 Apr 21.
PMID: 24753614
PUBLICATIONSDataCNSNeuroRegeneration
octubre 4, 2021
Sprouting of axonal collaterals after spinal cord injury is prevented by delayed axonal degeneration.
Collyer E, Catenaccio A, Lemaitre D, Diaz P, Valenzuela V, Bronfman F, Court FA.
Exp Neurol. 2014 Nov;261:451-61. doi: 10.1016/j.expneurol.2014.07.014. Epub 2014 Jul 28.
PMID: 25079366
PUBLICATIONSDataPNSCNSNeuroDegeneration
octubre 4, 2021
Trehalose delays the progression of amyotrophic lateral sclerosis by enhancing autophagy in motoneurons.
Castillo K, Nassif M, Valenzuela V, Rojas F, Matus S, Mercado G, Court FA, van Zundert B, Hetz C.
Autophagy. 2013 Sep;9(9):1308-20. doi: 10.4161/auto.25188. Epub 2013 Jun 6.
PMID: 23851366
PUBLICATIONSDataPNSCNSNeuroRegeneration
octubre 4, 2021
Activation of the unfolded protein response enhances motor recovery after spinal cord injury.
Valenzuela V, Collyer E, Armentano D, Parsons GB, Court FA, Hetz C.
Cell Death Dis. 2012 Feb 16;3(2):e272. doi: 10.1038/cddis.2012.8.
PMID: 22337234
PUBLICATIONSDataCNSNeuroRegeneration
octubre 4, 2021
Targeting the UPR transcription factor XBP1 protects against Huntington’s disease through the regulation of FoxO1 and autophagy.
Vidal RL, Figueroa A, Court FA, Thielen P, Molina C, Wirth C, Caballero B, Kiffin R, Segura-Aguilar J, Cuervo AM, Glimcher LH, Hetz C.
Hum Mol Genet. 2012 May 15;21(10):2245-62. doi: 10.1093/hmg/dds040. Epub 2012 Feb 14.
PMID: 22337954
PUBLICATIONSReviewPNSCNSNeuroDegeneration
octubre 4, 2021
Mitochondria as a central sensor for axonal degenerative stimuli.
Court FA, Coleman MP.
Trends Neurosci. 2012 Jun;35(6):364-72. doi: 10.1016/j.tins.2012.04.001. Epub 2012 May 11.
PMID: 22578891
PUBLICATIONSReviewNervous System FxPNSCNS
octubre 4, 2021
Slow axoplasmic transport under scrutiny.
Court FA, Alvarez J.
Biol Res. 2011;44(4):311-21. Epub 2012 Feb 10.
PMID: 22446593
PUBLICATIONSDataPNSCNSNeuroDegeneration
octubre 4, 2021
Axonal degeneration is mediated by the mitochondrial permeability transition pore.
Barrientos SA, Martinez NW, Yoo S, Jara JS, Zamorano S, Hetz C, Twiss JL, Alvarez J, Court FA.
J Neurosci. 2011 Jan 19;31(3):966-78. doi: 10.1523/JNEUROSCI.4065-10.2011.
PMID: 21248121
octubre 4, 2021
XBP-1 deficiency in the nervous system protects against amyotrophic lateral sclerosis by increasing autophagy
Hetz C, Thielen P, Matus S, Nassif M, Court F, Kiffin R, Martinez G, Cuervo AM, Brown RH, Glimcher LH.
Genes Dev. 2009 Oct 1;23(19):2294-306. doi: 10.1101/gad.1830709. Epub 2009 Sep 17.
PMID: 19762508
PUBLICATIONSDataPNSCNSNeuroDegeneration
septiembre 30, 2021
Progressive abnormalities in skeletal muscle and neuromuscular junctions of transgenic mice expressing the Huntington’s disease mutation.
Ribchester RR, Thomson D, Wood NI, Hinks T, Gillingwater TH, Wishart TM, Court FA, Morton AJ.
Eur J Neurosci. 2004 Dec;20(11):3092-114. doi: 10.1111/j.1460-9568.2004.03783.x.
PMID: 15579164
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